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Canis lupus familiaris (dog) Branched-chain amino acid catabolism (provided by Reactome)

18 gene

The longest variant of each gene is displayed. Click the see gene variants link to see all gene variants.


Gene Symbol Full Name
HSD17B10 hydroxysteroid 17-beta dehydrogenase 10
BBOX1 gamma-butyrobetaine hydroxylase 1
SHMT1 serine hydroxymethyltransferase 1
DLD dihydrolipoamide dehydrogenase
PPM1K protein phosphatase, Mg2+/Mn2+ dependent 1K
ACADSB acyl-CoA dehydrogenase short/branched chain
BCAT1 branched chain amino acid transaminase 1
ALDH9A1 aldehyde dehydrogenase 9 family member A1
DBT dihydrolipoamide branched chain transacylase E2
BCKDHB branched chain keto acid dehydrogenase E1 subunit beta
HIBCH 3-hydroxyisobutyryl-CoA hydrolase
HIBADH 3-hydroxyisobutyrate dehydrogenase
ACAD8 acyl-CoA dehydrogenase family member 8
ACAT1 acetyl-CoA acetyltransferase 1
MCCC1 methylcrotonoyl-CoA carboxylase 1
ALDH6A1 aldehyde dehydrogenase 6 family member A1
MCCC2 methylcrotonoyl-CoA carboxylase 2
TMLHE trimethyllysine hydroxylase, epsilon
ORF