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  • Entrez Gene ID (e.g. 7157)
  • gene symbol (e.g. TP53)
  • gene name (e.g. tumor protein p53)
  • gene synonyms (e.g. FLJ92943)
  • Ensembl ID (e.g. ENSG0000141510)
  • Accession No. (e.g. NM_000546)
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Homo sapiens (human) Amino Acid metabolism (provided by WikiPathways)

91 gene

The longest variant of each gene is displayed. Click the see gene variants link to see all gene variants.


Gene Symbol Full Name
TPO thyroid peroxidase
PC pyruvate carboxylase
P4HA2 prolyl 4-hydroxylase subunit alpha 2
GSS glutathione synthetase
SMS spermine synthase
HNMT histamine N-methyltransferase
PKM pyruvate kinase M1/2
PPM1L protein phosphatase, Mg2+/Mn2+ dependent 1L
ARG1 arginase 1
ADH1C alcohol dehydrogenase 1C (class I), gamma polypeptide
BHMT betaine--homocysteine S-methyltransferase
MDH2 malate dehydrogenase 2
G6PC2 glucose-6-phosphatase catalytic subunit 2
DLST dihydrolipoamide S-succinyltransferase
OAT ornithine aminotransferase
TH tyrosine hydroxylase
SRM spermidine synthase
SDS serine dehydratase
DLD dihydrolipoamide dehydrogenase
LARS2 leucyl-tRNA synthetase 2, mitochondrial
ASS1 argininosuccinate synthase 1
PYCR1 pyrroline-5-carboxylate reductase 1
GSR glutathione-disulfide reductase
ACSS1 acyl-CoA synthetase short chain family member 1
ACAA1 acetyl-CoA acyltransferase 1
ALDH18A1 aldehyde dehydrogenase 18 family member A1
DDC dopa decarboxylase
IDH1 isocitrate dehydrogenase (NADP(+)) 1, cytosolic
CBS cystathionine-beta-synthase
GOT1 glutamic-oxaloacetic transaminase 1
OGDH oxoglutarate dehydrogenase
ADH4 alcohol dehydrogenase 4 (class II), pi polypeptide
MAOA monoamine oxidase A
CTH cystathionine gamma-lyase
TAT tyrosine aminotransferase
ACADM acyl-CoA dehydrogenase medium chain
HIBCH 3-hydroxyisobutyryl-CoA hydrolase
CPS1 carbamoyl-phosphate synthase 1
VARS valyl-tRNA synthetase
ODC1 ornithine decarboxylase 1
GOT2 glutamic-oxaloacetic transaminase 2
OTC ornithine carbamoyltransferase
HMGCL 3-hydroxymethyl-3-methylglutaryl-CoA lyase
AUH AU RNA binding methylglutaconyl-CoA hydratase
AOC3 amine oxidase, copper containing 3
PNMT phenylethanolamine N-methyltransferase
ADH7 alcohol dehydrogenase 7 (class IV), mu or sigma polypeptide
HIBADH 3-hydroxyisobutyrate dehydrogenase
TPH1 tryptophan hydroxylase 1
GCLM glutamate-cysteine ligase modifier subunit
MDH1 malate dehydrogenase 1
IARS isoleucyl-tRNA synthetase
ALDH7A1 aldehyde dehydrogenase 7 family member A1
GPT2 glutamic--pyruvic transaminase 2
HADH hydroxyacyl-CoA dehydrogenase
CAD carbamoyl-phosphate synthetase 2, aspartate transcarbamylase, and dihydroorotase
ARG2 arginase 2
FH fumarate hydratase
PDHA1 pyruvate dehydrogenase E1 alpha 1 subunit
GLS glutaminase
MCCC1 methylcrotonoyl-CoA carboxylase 1
FTCD formimidoyltransferase cyclodeaminase
WARS tryptophanyl-tRNA synthetase
DBH dopamine beta-hydroxylase
ALDH1A1 aldehyde dehydrogenase 1 family member A1
ADH5 alcohol dehydrogenase 5 (class III), chi polypeptide
GLUD1 glutamate dehydrogenase 1
PCK1 phosphoenolpyruvate carboxykinase 1
BCAT1 branched chain amino acid transaminase 1
MUT methylmalonyl-CoA mutase
ACO2 aconitase 2
HMGCS2 3-hydroxy-3-methylglutaryl-CoA synthase 2
HAL histidine ammonia-lyase
TDO2 tryptophan 2,3-dioxygenase
ACLY ATP citrate lyase
FARSB phenylalanyl-tRNA synthetase beta subunit
HDC histidine decarboxylase
GLUL glutamate-ammonia ligase
MARS2 methionyl-tRNA synthetase 2, mitochondrial
PDK4 pyruvate dehydrogenase kinase 4
PDHX pyruvate dehydrogenase complex component X
SUCLG1 succinate-CoA ligase alpha subunit
ASNS asparagine synthetase (glutamine-hydrolyzing)
EHHADH enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase
FAH fumarylacetoacetate hydrolase
EPRS glutamyl-prolyl-tRNA synthetase
MPST mercaptopyruvate sulfurtransferase
CS citrate synthase
LDHA lactate dehydrogenase A
SDHA succinate dehydrogenase complex flavoprotein subunit A
RARS arginyl-tRNA synthetase