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Homo sapiens (human) Complex I biogenesis (provided by Reactome)

57 gene

The longest variant of each gene is displayed. Click the see gene variants link to see all gene variants.


Gene Symbol Full Name
MIR4691 microRNA 4691
NDUFV1 NADH:ubiquinone oxidoreductase core subunit V1
NDUFA8 NADH:ubiquinone oxidoreductase subunit A8
NDUFAF3 NADH:ubiquinone oxidoreductase complex assembly factor 3
NDUFS5 NADH:ubiquinone oxidoreductase subunit S5
NDUFS7 NADH:ubiquinone oxidoreductase core subunit S7
TIMMDC1 translocase of inner mitochondrial membrane domain containing 1
NDUFB2 NADH:ubiquinone oxidoreductase subunit B2
NDUFS3 NADH:ubiquinone oxidoreductase core subunit S3
NDUFS2 NADH:ubiquinone oxidoreductase core subunit S2
NDUFS8 NADH:ubiquinone oxidoreductase core subunit S8
NDUFV3 NADH:ubiquinone oxidoreductase subunit V3
ND2 MTND2
ND5 NADH dehydrogenase, subunit 5 (complex I)
NDUFB5 NADH:ubiquinone oxidoreductase subunit B5
NDUFA2 NADH:ubiquinone oxidoreductase subunit A2
ACAD9 acyl-CoA dehydrogenase family member 9
NDUFB11 NADH:ubiquinone oxidoreductase subunit B11
NDUFA1 NADH:ubiquinone oxidoreductase subunit A1
NDUFA11 NADH:ubiquinone oxidoreductase subunit A11
NDUFC1 NADH:ubiquinone oxidoreductase subunit C1
ND1 NADH dehydrogenase, subunit 1 (complex I)
NDUFB3 NADH:ubiquinone oxidoreductase subunit B3
ECSIT ECSIT signalling integrator
NDUFB6 NADH:ubiquinone oxidoreductase subunit B6
NDUFA9 NADH:ubiquinone oxidoreductase subunit A9
NDUFS1 NADH:ubiquinone oxidoreductase core subunit S1
NDUFS6 NADH:ubiquinone oxidoreductase subunit S6
NDUFA6 NADH:ubiquinone oxidoreductase subunit A6
TMEM126B transmembrane protein 126B
NDUFAB1 NADH:ubiquinone oxidoreductase subunit AB1
NDUFAF7 NADH:ubiquinone oxidoreductase complex assembly factor 7
NDUFB7 NADH:ubiquinone oxidoreductase subunit B7
NDUFB8 NADH:ubiquinone oxidoreductase subunit B8
NUBPL nucleotide binding protein like
NDUFA13 NADH:ubiquinone oxidoreductase subunit A13
NDUFB4 NADH:ubiquinone oxidoreductase subunit B4
ND3 NADH dehydrogenase, subunit 3 (complex I)
NDUFA7 NADH:ubiquinone oxidoreductase subunit A7
NDUFA5 NADH:ubiquinone oxidoreductase subunit A5
NDUFA10 NADH:ubiquinone oxidoreductase subunit A10
NDUFC2 NADH:ubiquinone oxidoreductase subunit C2
NDUFB10 NADH:ubiquinone oxidoreductase subunit B10
NDUFA3 NADH:ubiquinone oxidoreductase subunit A3
ND4 NADH dehydrogenase, subunit 4 (complex I)
ND6 NADH dehydrogenase, subunit 6 (complex I)
NDUFV2 NADH:ubiquinone oxidoreductase core subunit V2
NDUFAF5 NADH:ubiquinone oxidoreductase complex assembly factor 5
NDUFA12 NADH:ubiquinone oxidoreductase subunit A12
NDUFB9 NADH:ubiquinone oxidoreductase subunit B9
NDUFB1 NADH:ubiquinone oxidoreductase subunit B1
MIR7113 microRNA 7113
NDUFAF6 NADH:ubiquinone oxidoreductase complex assembly factor 6
NDUFAF1 NADH:ubiquinone oxidoreductase complex assembly factor 1
NDUFAF2 NADH:ubiquinone oxidoreductase complex assembly factor 2
NDUFS4 NADH:ubiquinone oxidoreductase subunit S4
NDUFAF4 NADH:ubiquinone oxidoreductase complex assembly factor 4
ORF